Cortical murine neurons lacking the neurofilament light chain protein have an attenuated response to injury in vitro

J Neurotrauma. 2013 Nov 15;30(22):1908-18. doi: 10.1089/neu.2013.2850.

Abstract

Neurofilaments (NFs) have been proposed to have a significant role in attempted axonal regeneration following a variety of forms of injury. The NF triplet proteins of the central nervous system are comprised of light (NF-L), medium (NF-M) and heavy (NF-H) chains and are part of the type IV intermediate filament family. We sought to define the role of NF-L in the neuronal response to trauma and regeneration by examining the effect of total absence of the NF-L protein on neuronal maturation and response to axotomy. This study utilized an in vitro model comprising relatively mature cortical murine neurons derived from either wild-type embryonic (E15) mice or mice with a genetic knockout of NF-L (NF-L KO). Whilst NF-L KO neurons developed to relative maturity at a comparable rate to wild-type control neurons, NF-L KO neurons demonstrated relatively increased expression of α-internexin and decreased expression of NF-M. Further, we demonstrate that α-internexin co-immunoprecipitates with the NF binding protein NDel1 in NFL-KO cortical neurons in vitro. Following localized axotomy, NF-L KO neurons demonstrated reduced amyloid precursor protein accumulation in damaged neurites as well as a significant reduction in the number of axons regenerating (4.79+/-0.58 sprouts) in comparison to control preparations (10.47+/-1.11 sprouts) (p<0.05). These studies indicate that NFs comprising NF-L have a dynamic role in the reactive and regenerative changes in axons following injury.

MeSH terms

  • Animals
  • Axons / metabolism*
  • Axons / pathology
  • Axotomy
  • Carrier Proteins / metabolism
  • Cerebral Cortex / cytology
  • Cerebral Cortex / metabolism
  • Embryo, Mammalian
  • Intermediate Filament Proteins / metabolism
  • Mice
  • Mice, Inbred C57BL
  • Mice, Knockout
  • Neurofilament Proteins / metabolism*
  • Neurons / metabolism*

Substances

  • Carrier Proteins
  • Intermediate Filament Proteins
  • Ndel1 protein, mouse
  • Neurofilament Proteins
  • alpha-internexin
  • neurofilament protein L
  • neurofilament protein M