Primary multicentric anaplastic pleomorphic xanthoastrocytoma with atypical features

J Clin Neurosci. 2013 Nov;20(11):1605-8. doi: 10.1016/j.jocn.2012.09.046. Epub 2013 Jul 1.

Abstract

Pleomorphic xanthoastrocytoma (PXA) is a rare tumor with good prognosis after surgery. Few cases of anaplastic PXA (either de novo or secondary to transformation of a recurrent low grade PXA) have been reported. Moreover, primary anaplastic PXA with dissemination at diagnosis has been described only in two patients, to our knowledge. We report the first case of primary multicentric anaplastic PXA and discuss its atypical features and the pertinent literature.

Keywords: Anaplastic pleomorphic xanthoastrocytoma; MRI; PXA; Prognosis; Radiotherapy; Surgery.

Publication types

  • Case Reports

MeSH terms

  • Astrocytoma / pathology*
  • Astrocytoma / surgery
  • Brain Neoplasms / pathology*
  • Brain Neoplasms / surgery
  • Humans
  • Male
  • Young Adult