Chromosomal translocations involving the IGH@ locus in B-cell precursor acute lymphoblastic leukemia: 29 new cases and a review of the literature

Cancer Genet. 2013 May;206(5):162-73. doi: 10.1016/j.cancergen.2013.04.004. Epub 2013 Jul 1.

Abstract

Chromosomal translocations involving the immunoglobulin heavy chain locus (IGH@) are recurrent but rare in B-cell precursor acute lymphoblastic leukemia (BCP-ALL), and various partner genes have been described. Here, we report a new series of 29 cases of BCP-ALL with IGH@ translocations. The partner gene was identified by fluorescence in situ hybridization and/or molecular cloning in 20 patients. Members of the CEBP gene family (n = 11), BCL2 (n = 3), ID4 (n = 3), EPOR (n = 2), and TRA/D@ (n = 1) were identified and demonstrated by quantitative real-time reverse transcriptase-polymerase chain reaction to be markedly up-regulated. The present cases, added to those already reported, confirm the diversity of the partner genes, which, apart from BCL2, are specific to BCP-ALL. Collectively, patients with IGH@ translocations may represent a novel sub-group of BCP-ALL occurring in adolescents and young adults.

Keywords: B-cell progenitor acute lymphoblastic leukemia; IGH@ translocations.

Publication types

  • Review

MeSH terms

  • Adolescent
  • Adult
  • Aged
  • Aged, 80 and over
  • CCAAT-Enhancer-Binding Proteins / genetics
  • Child
  • Child, Preschool
  • Chromosomes, Human, Pair 14
  • Cloning, Molecular
  • Female
  • Humans
  • Immunoglobulin Heavy Chains / genetics*
  • In Situ Hybridization, Fluorescence
  • Inhibitor of Differentiation Proteins / genetics
  • Male
  • Middle Aged
  • Precursor Cell Lymphoblastic Leukemia-Lymphoma / genetics*
  • Proto-Oncogene Proteins c-bcl-2 / genetics
  • Real-Time Polymerase Chain Reaction
  • Receptors, Erythropoietin / genetics
  • Translocation, Genetic*

Substances

  • CCAAT-Enhancer-Binding Proteins
  • ID4 protein, human
  • Immunoglobulin Heavy Chains
  • Inhibitor of Differentiation Proteins
  • Proto-Oncogene Proteins c-bcl-2
  • Receptors, Erythropoietin