Distinct phenotypes of children with perianal perforating Crohn's disease

J Pediatr Surg. 2013 Jun;48(6):1301-5. doi: 10.1016/j.jpedsurg.2013.03.027.

Abstract

Purpose: Perianal perforating disease (PF) has been reported in approximately 15% of children with Crohn's disease (CD). It is unknown whether children who present with PF at the time of diagnosis have a different course than those that develop PF while on therapy.

Methods: From a prospective, single institution observational registry of children diagnosed with CD, we identified children with perianal perforating CD, defined as perianal abscesses and/or fistulae. Patients who presented with perianal perforating CD (PF-CD0) were compared to those who developed perianal perforating CD (PF-CD1) after initial diagnosis.

Results: Thirty-eight of 215 (18%) children with CD had PF-CD during a median follow up of 4.5 years. Patients with PF-CD0 (n=26) tended to be more likely male (81% vs. 50%, p=0.07) and younger (9.3 yrs vs. 12.5 yrs, p=0.02). PF-CD1 (n=12) patients were more likely to require diverting ileostomy (42% vs. 8%, p=0.02) and colectomy (33% vs. 4%, p=0.03). Multivariable analysis predicted increased rate of diverting ileostomy in the PF-CD1 group (p=0.007, OR 19.1, 95% CI 1.6-234.8).

Conclusion: Pediatric CD patients who develop PF while on therapy for CD have a more severe phenotype and are more likely to require diverting ileostomy or colectomy compared to those who present with PF-CD.

Keywords: Crohn’s disease; Inflammatory bowel disease; Perforating; Perianal Crohn’s disease; Seton.

Publication types

  • Observational Study

MeSH terms

  • Abscess / etiology*
  • Abscess / surgery
  • Adolescent
  • Anti-Inflammatory Agents / therapeutic use
  • Anus Diseases / etiology*
  • Anus Diseases / surgery
  • Child
  • Child, Preschool
  • Colectomy / statistics & numerical data
  • Combined Modality Therapy
  • Crohn Disease / complications*
  • Crohn Disease / diagnosis
  • Crohn Disease / drug therapy
  • Crohn Disease / surgery
  • Disease Progression
  • Female
  • Follow-Up Studies
  • Humans
  • Ileostomy / statistics & numerical data
  • Logistic Models
  • Male
  • Multivariate Analysis
  • Phenotype*
  • Prognosis
  • Prospective Studies
  • Rectal Fistula / etiology*
  • Rectal Fistula / surgery
  • Registries
  • Risk Factors
  • Treatment Outcome

Substances

  • Anti-Inflammatory Agents

Supplementary concepts

  • Pediatric Crohn's disease