WIP1, a homeostatic regulator of the DNA damage response, is targeted by HIPK2 for phosphorylation and degradation

Mol Cell. 2013 Aug 8;51(3):374-85. doi: 10.1016/j.molcel.2013.06.010. Epub 2013 Jul 18.

Abstract

WIP1 (wild-type p53-induced phosphatase 1) functions as a homeostatic regulator of the ataxia telangiectasia mutated (ATM)-mediated signaling pathway in response to ionizing radiation (IR). Here we identify homeodomain-interacting protein kinase 2 (HIPK2) as a protein kinase that targets WIP1 for phosphorylation and proteasomal degradation. In unstressed cells, WIP1 is constitutively phosphorylated by HIPK2 and maintained at a low level by proteasomal degradation. In response to IR, ATM-dependent AMPKα2-mediated HIPK2 phosphorylation promotes inhibition of WIP1 phosphorylation through dissociation of WIP1 from HIPK2, followed by stabilization of WIP1 for termination of the ATM-mediated double-strand break (DSB) signaling cascade. Notably, HIPK2 depletion impairs IR-induced γ-H2AX foci formation, cell-cycle checkpoint activation, and DNA repair signaling, and the survival rate of hipk2+/- mice upon γ-irradiation is markedly reduced compared to wild-type mice. Taken together, HIPK2 plays a critical role in the initiation of DSB repair signaling by controlling WIP1 levels in response to IR.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • AMP-Activated Protein Kinases / metabolism
  • Animals
  • Carrier Proteins / metabolism*
  • Cell Cycle Checkpoints
  • Cell Line, Tumor
  • DNA Damage / genetics
  • DNA Damage / radiation effects*
  • DNA Repair*
  • HEK293 Cells
  • HeLa Cells
  • Histones / metabolism
  • Humans
  • Mice
  • Mice, Transgenic
  • Phosphoprotein Phosphatases / metabolism*
  • Phosphorylation
  • Protein Phosphatase 2C
  • Protein Serine-Threonine Kinases / metabolism*
  • Radiation, Ionizing
  • Signal Transduction
  • Ubiquitination

Substances

  • Carrier Proteins
  • H2AX protein, human
  • Histones
  • HIPK2 protein, human
  • PRKAA2 protein, human
  • Protein Serine-Threonine Kinases
  • AMP-Activated Protein Kinases
  • PPM1D protein, human
  • Phosphoprotein Phosphatases
  • Ppm1d protein, mouse
  • Protein Phosphatase 2C