Chondrocyte-specific inhibition of β-catenin signaling leads to dysplasia of the caudal vertebrae in mice

Spine (Phila Pa 1976). 2013 Nov 15;38(24):2079-84. doi: 10.1097/01.brs.0000435024.57940.8d.

Abstract

Study design: To inhibit β-catenin specifically signaling in chondrocytes Col2-ICAT transgenic mice were generated. Anomalies in caudal vertebrae were detected during embryonic and postnatal stages of Col2-ICAT transgenic mice.

Objective: To determine the role of canonical β-catenin signaling in caudal vertebral development.

Summary of background data: β-catenin signaling plays a critical role in skeletal development. Col2-ICAT transgenic mice were generated to selectively block β-catenin signaling by overexpression of the ICAT gene in chondrocytes.

Methods: Tails of E16.5 transgenic embryos and adult Col2-ICAT transgenic mice and their wild-type littermates were collected and analyzed. Skeletal preparation, 3-dimensional micro-computed tomographic and histological analyses were performed to evaluate changes in the structure of caudal vertebrae. Bromodeoxyuridine labeling was performed to evaluate changes in chondrocyte proliferation in caudal vertebrae.

Results: Skeletal preparation and 3-dimensional micro-computed tomographic analyses revealed bone deformation and angulated deformities in tail tissue in Col2-ICAT transgenic mice. Histological studies revealed abnormal bone development and dysplastic caudal vertebrae in Col2-ICAT transgenic mice. Inhibition of β-catenin signaling in cartilage resulted in vertebral dysplasia leading to aberrant resegmenting process. Thus, 2 poorly developed sclerotomes failed to fuse to form a complete vertebrae. BrdU labeling revealed a decreased chondrocyte proliferation in both cartilageous templates of transgenic embryos and the growth plate of adult Col2-ICAT transgenic mice.

Conclusion: Wnt/β-catenin signaling plays an important role in vertebral development. Inhibition of β-catenin signaling in chondrocytes results in caudal vertebra deformity in mice, which may occur as early as in the stage of sclerotome formation.

Level of evidence: N/A.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adaptor Proteins, Signal Transducing
  • Animals
  • Cell Cycle Proteins / genetics
  • Cell Cycle Proteins / metabolism
  • Cell Proliferation
  • Chondrocytes / cytology
  • Chondrocytes / metabolism*
  • Collagen Type II / genetics
  • Embryo, Mammalian / abnormalities
  • Embryo, Mammalian / metabolism
  • Enhancer Elements, Genetic / genetics
  • Immunohistochemistry
  • Mice
  • Mice, Inbred C57BL
  • Mice, Transgenic
  • Promoter Regions, Genetic / genetics
  • Repressor Proteins
  • Signal Transduction*
  • Spine / abnormalities
  • Spine / diagnostic imaging
  • Spine / metabolism*
  • Tail / abnormalities
  • Tail / diagnostic imaging
  • Tail / metabolism
  • Transcription Factors / genetics
  • Transcription Factors / metabolism
  • X-Ray Microtomography
  • beta Catenin / genetics
  • beta Catenin / metabolism*

Substances

  • Adaptor Proteins, Signal Transducing
  • Cell Cycle Proteins
  • Col2a1 protein, mouse
  • Collagen Type II
  • Ctnnbip1 protein, mouse
  • Repressor Proteins
  • Transcription Factors
  • beta Catenin