Neuroblastoma, a tumor of the sympathetic nervous system, accounts for 8 percent of all pediatric tumors and causes 11 percent of all deaths from cancer in children. Patients with this tumor usually present with symptoms before four years of age; neuroblastoma rarely occurs after 14 years of age. Clinical manifestations vary, depending on tumor site and extent of the tumor. The case described here illustrates the main features of presentation, diagnosis and treatment.