An epidermal microRNA regulates neuronal migration through control of the cellular glycosylation state

Science. 2013 Sep 20;341(6152):1404-8. doi: 10.1126/science.1242528.

Abstract

An appropriate balance in glycosylation of proteoglycans is crucial for their ability to regulate animal development. Here, we report that the Caenorhabditis elegans microRNA mir-79, an ortholog of mammalian miR-9, controls sugar-chain homeostasis by targeting two proteins in the proteoglycan biosynthetic pathway: a chondroitin synthase (SQV-5; squashed vulva-5) and a uridine 5'-diphosphate-sugar transporter (SQV-7). Loss of mir-79 causes neurodevelopmental defects through SQV-5 and SQV-7 dysregulation in the epidermis. This results in a partial shutdown of heparan sulfate biosynthesis that impinges on a LON-2/glypican pathway and disrupts neuronal migration. Our results identify a regulatory axis controlled by a conserved microRNA that maintains proteoglycan homeostasis in cells.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Caenorhabditis elegans / metabolism
  • Caenorhabditis elegans / physiology*
  • Caenorhabditis elegans Proteins / biosynthesis
  • Caenorhabditis elegans Proteins / genetics
  • Caenorhabditis elegans Proteins / metabolism
  • Cell Movement*
  • Epidermis / metabolism*
  • Glycosylation
  • Glycosyltransferases / metabolism
  • Glypicans / biosynthesis
  • Glypicans / genetics
  • Heparan Sulfate Proteoglycans / biosynthesis*
  • Heparan Sulfate Proteoglycans / genetics
  • MicroRNAs / genetics
  • MicroRNAs / physiology*
  • Monosaccharide Transport Proteins / metabolism
  • Neurons / physiology*
  • Nucleobase, Nucleoside, Nucleotide, and Nucleic Acid Transport Proteins / metabolism

Substances

  • Caenorhabditis elegans Proteins
  • Glypicans
  • Heparan Sulfate Proteoglycans
  • LON-2 protein, C elegans
  • MIRN79 microRNA, C elegans
  • MicroRNAs
  • Monosaccharide Transport Proteins
  • Nucleobase, Nucleoside, Nucleotide, and Nucleic Acid Transport Proteins
  • sqv-7 protein, C elegans
  • Glycosyltransferases
  • sqv-5 protein, C elegans