Malignant teratoid ciliary body medulloepithelioma in a neonate

J Pediatr Ophthalmol Strabismus. 2013 Aug 6:50 Online:e37-40. doi: 10.3928/01913913-20130730-01.

Abstract

Ciliary body medulloepithelioma is an intraocular tumor manifesting in early childhood, rarely at birth. A unique case of intraocular malignant teratoid ciliary body medulloepithelioma in a neonate presenting as buphthalmos at birth is reported. There was rapid progression with extraocular extension within 2 months and developed regional lymph node metastasis despite enucleation. The child underwent lymph node dissection and local radiotherapy with complete remission.

Publication types

  • Case Reports

MeSH terms

  • Calcinosis / diagnostic imaging
  • Ciliary Body / diagnostic imaging
  • Ciliary Body / pathology*
  • Ciliary Body / radiation effects
  • Eye Enucleation
  • Female
  • Gestational Age
  • Humans
  • Hydrophthalmos / diagnosis
  • Infant, Newborn
  • Infant, Premature
  • Intraocular Pressure
  • Lymph Node Excision
  • Lymphatic Metastasis
  • Neuroectodermal Tumors, Primitive / diagnostic imaging
  • Neuroectodermal Tumors, Primitive / radiotherapy
  • Neuroectodermal Tumors, Primitive / secondary*
  • Tomography, X-Ray Computed
  • Ultrasonography
  • Uveal Neoplasms / diagnostic imaging
  • Uveal Neoplasms / pathology*
  • Uveal Neoplasms / radiotherapy