Unexplained double-chambered left ventricle associated with contracting right ventricular aneurysm and right atrial enlargement

Gherardo Finocchiaro; Daniel Murphy; Aleksandra Pavlovic; Francois Haddad; Hadas Shiran; Gianfranco Sinagra; Euan A Ashley; Joshua W Knowles

doi:10.1111/echo.12467

Unexplained double-chambered left ventricle associated with contracting right ventricular aneurysm and right atrial enlargement

Echocardiography. 2014 Mar;31(3):E80-4. doi: 10.1111/echo.12467. Epub 2013 Dec 3.

Authors

Gherardo Finocchiaro¹, Daniel Murphy, Aleksandra Pavlovic, Francois Haddad, Hadas Shiran, Gianfranco Sinagra, Euan A Ashley, Joshua W Knowles

Affiliation

¹ Division of Cardiovascular Medicine, Department of Medicine, Stanford University School of Medicine, Stanford, California.

PMID: 24299065
DOI: 10.1111/echo.12467

Abstract

In this article, we describe a double-chambered left ventricle (LV) associated with a functional right ventricular (RV) aneurysm and right atrial (RA) enlargement in an asymptomatic 24-year-old woman with a family history of sudden cardiac death. We will discuss the differential diagnosis, genetic testing and possible prognostic implications.

Keywords: congenital heart disease; double-chambered left ventricle.

Publication types

Case Reports

MeSH terms

Abnormalities, Multiple / diagnosis
Abnormalities, Multiple / therapy
Angiotensin-Converting Enzyme Inhibitors / therapeutic use
Cardiomegaly / diagnosis*
Cardiomegaly / drug therapy
Echocardiography / methods*
Female
Follow-Up Studies
Heart Aneurysm / diagnosis*
Heart Atria
Heart Defects, Congenital / diagnosis
Heart Defects, Congenital / therapy
Heart Ventricles / abnormalities*
Humans
Magnetic Resonance Imaging, Cine / methods*
Multimodal Imaging / methods
Risk Assessment
Severity of Illness Index
Stroke Volume
Young Adult

Substances

Angiotensin-Converting Enzyme Inhibitors