E3 ubiquitin ligase Cbl-b suppresses proallergic T cell development and allergic airway inflammation

Cell Rep. 2014 Feb 27;6(4):709-23. doi: 10.1016/j.celrep.2014.01.012. Epub 2014 Feb 6.

Abstract

E3 ubiquitin ligase Cbl-b has emerged as a gatekeeper that controls the activation threshold of the T cell antigen receptor and maintains the balance between tolerance and autoimmunity. Here, we report that the loss of Cbl-b facilitates T helper 2 (Th2) and Th9 cell differentiation in vitro. In a mouse model of asthma, the absence of Cbl-b results in severe airway inflammation and stronger Th2 and Th9 responses. Mechanistically, Cbl-b selectively associates with Stat6 upon IL-4 ligation and targets Stat6 for ubiquitination and degradation. These processes are heightened in the presence of T cell receptor (TCR)/CD28 costimulation. Furthermore, we identify K108 and K398 as Stat6 ubiquitination sites. Intriguingly, introducing Stat6 deficiency into Cblb(-/-) mice abrogates hyper-Th2 responses but only partially attenuates Th9 responses. Therefore, our data reveal a function for Cbl-b in the regulation of Th2 and Th9 cell differentiation.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adaptor Proteins, Signal Transducing / genetics
  • Adaptor Proteins, Signal Transducing / metabolism*
  • Animals
  • Asthma / immunology
  • Asthma / metabolism*
  • CD28 Antigens / metabolism
  • Cell Differentiation*
  • Interleukin-4 / metabolism
  • Mice
  • Mice, Inbred BALB C
  • Proteolysis
  • Proto-Oncogene Proteins c-cbl / genetics
  • Proto-Oncogene Proteins c-cbl / metabolism*
  • STAT6 Transcription Factor / genetics
  • STAT6 Transcription Factor / metabolism
  • Th2 Cells / cytology
  • Th2 Cells / immunology
  • Th2 Cells / metabolism*
  • Ubiquitination

Substances

  • Adaptor Proteins, Signal Transducing
  • CD28 Antigens
  • Cblb protein, mouse
  • STAT6 Transcription Factor
  • Stat6 protein, mouse
  • Interleukin-4
  • Proto-Oncogene Proteins c-cbl