Interleukin-6 (IL-6) trans signaling drives a STAT3-dependent pathway that leads to hyperactive transforming growth factor-β (TGF-β) signaling promoting SMAD3 activation and fibrosis via Gremlin protein

J Biol Chem. 2014 Apr 4;289(14):9952-60. doi: 10.1074/jbc.M113.545822. Epub 2014 Feb 18.

Abstract

Fibrosis is a common and intractable condition associated with various pathologies. It is characterized by accumulation of an excessive amount of extracellular matrix molecules that primarily include collagen type I. IL-6 is a profibrotic cytokine that is elevated in the prototypic fibrotic autoimmune condition systemic sclerosis and is known to induce collagen I expression, but the mechanism(s) behind this induction are currently unknown. Using healthy dermal fibroblasts in vitro, we analyzed the signaling pathways that underscore the IL-6-mediated induction of collagen. We show that IL-6 trans signaling is important and that the effect is dependent on STAT3; however, the effect is indirect and mediated through enhanced TGF-β signaling and the classic downstream cellular mediator Smad3. This is due to induction of the bone morphogenetic protein (BMP) antagonist Gremlin-1, and we show that Gremlin-1 is profibrotic and is mediated through canonical TGF-β signaling.

Keywords: Cell Biology; Collagen; Extracellular; Fibrogenesis; Interleukin; Interleukin-6; Signal Transduction.

Publication types

  • Clinical Trial

MeSH terms

  • Bone Morphogenetic Proteins / biosynthesis
  • Bone Morphogenetic Proteins / genetics
  • Cells, Cultured
  • Collagen Type I / biosynthesis
  • Collagen Type I / genetics
  • Female
  • Fibroblasts / metabolism*
  • Fibroblasts / pathology
  • Fibrosis / genetics
  • Fibrosis / metabolism
  • Fibrosis / pathology
  • Humans
  • Intercellular Signaling Peptides and Proteins / genetics
  • Intercellular Signaling Peptides and Proteins / metabolism*
  • Interleukin-6 / genetics
  • Interleukin-6 / metabolism*
  • STAT3 Transcription Factor / genetics
  • STAT3 Transcription Factor / metabolism*
  • Signal Transduction*
  • Smad3 Protein / genetics
  • Smad3 Protein / metabolism*
  • Transforming Growth Factor beta / genetics
  • Transforming Growth Factor beta / metabolism*

Substances

  • Bone Morphogenetic Proteins
  • Collagen Type I
  • GREM1 protein, human
  • IL6 protein, human
  • Intercellular Signaling Peptides and Proteins
  • Interleukin-6
  • SMAD3 protein, human
  • STAT3 Transcription Factor
  • STAT3 protein, human
  • Smad3 Protein
  • Transforming Growth Factor beta