Activated IL-22 pathway occurs in the muscle tissues of patients with polymyositis or dermatomyositis and is correlated with disease activity

Rheumatology (Oxford). 2014 Jul;53(7):1307-12. doi: 10.1093/rheumatology/keu005. Epub 2014 Mar 5.

Abstract

Objective: The aim of this study was to assess the expression of IL-22, IL-22 receptor 1 (IL-22R1), IL-22 binding protein (IL-22BP) and p-STAT3 in muscle tissue from patients with PM and DM.

Methods: Levels of IL-22, IL-22R1, IL-22BP and STAT3 mRNA were quantified by RT-PCR. The expression of IL-22, IL-22R1, IL-22BP and p-STAT3 was also analysed using immunohistochemistry.

Results: Significant modulation of the IL-22 pathway was observed in inflammatory myopathic tissues. In particular, a significant overexpression of IL-22 at the protein but not the mRNA level was observed in PM/DM tissues and was correlated with myositis activity. IL-22R1 aberrant expression was also observed among infiltrating mononuclear cells and necrotic muscle cells. IL-22BP, which inhibits IL-22 signalling, was expressed only in some muscle fibres in PM/DM patients.

Conclusion: Our findings indicate that the IL-22 pathway is activated in inflammatory myopathic tissues and may be involved in the induction of muscle inflammatory processes and muscle necrosis.

Keywords: IL-17; IL-22; IL-22R1; dermatomyositis; p-STAT3; polymyositis.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Biopsy
  • Case-Control Studies
  • Dermatomyositis / metabolism*
  • Dermatomyositis / pathology
  • Dermatomyositis / physiopathology
  • Humans
  • Inflammation / metabolism
  • Inflammation / pathology
  • Inflammation / physiopathology
  • Interleukin-22
  • Interleukins / metabolism*
  • Muscle, Skeletal / metabolism*
  • Muscle, Skeletal / pathology
  • Muscle, Skeletal / physiopathology
  • Necrosis / metabolism
  • Necrosis / pathology
  • Necrosis / physiopathology
  • Polymyositis / metabolism*
  • Polymyositis / pathology
  • Polymyositis / physiopathology
  • RNA, Messenger / metabolism
  • Receptors, Interleukin / metabolism
  • STAT3 Transcription Factor / metabolism
  • Severity of Illness Index*
  • Signal Transduction / physiology*

Substances

  • IL22RA2 protein, human
  • Interleukins
  • RNA, Messenger
  • Receptors, Interleukin
  • STAT3 Transcription Factor
  • STAT3 protein, human
  • interleukin-22 receptor