Influence of a two-year steroid treatment on body composition as measured by dual X-ray absorptiometry in boys with Duchenne muscular dystrophy

Neuromuscul Disord. 2014 Jun;24(6):467-73. doi: 10.1016/j.nmd.2014.03.002. Epub 2014 Mar 12.

Abstract

Steroids are nowadays routinely used as a long-term treatment in Duchenne muscular dystrophy (DMD). Their effects on body composition were assessed using dual X-ray absorptiometry. The study followed over 2 years 29 genetically confirmed DMD patients: 21 in the steroid-treated group and 8 in the steroid-naïve group. After 2 years of steroid treatment, the lean tissue mass values increased significantly (p<0.0001), the percentage of body fat mass remained practically constant (p=0.94) in comparison with the initial visit. In the steroid-naïve patients, there were no significant increases in the lean tissue mass but deterioration in body composition confirmed by a significant increase in the percentage of body fat mass. Besides, significant negative correlations were found between the percentage of body fat mass and the MFM total score (R=-0.79, n=76, p<0.0001). A 2-year steroid treatment improves significantly body composition of boys with DMD through a significant increase in lean tissue mass. We suggest that a thorough check of body composition should be carried out before steroid treatment discontinuation in case of overweight gain.

Keywords: Body composition; Duchenne muscular dystrophy; Steroids.

MeSH terms

  • Absorptiometry, Photon
  • Adolescent
  • Body Composition / drug effects*
  • Child
  • Child, Preschool
  • Humans
  • Male
  • Motor Activity / drug effects
  • Muscular Dystrophy, Duchenne / diagnostic imaging
  • Muscular Dystrophy, Duchenne / drug therapy*
  • Steroids / administration & dosage
  • Steroids / therapeutic use*

Substances

  • Steroids