Clinical aspects of portopulmonary hypertension

Boris I Medarov; Amit Chopra; Marc A Judson

doi:10.1016/j.rmed.2014.04.004

Clinical aspects of portopulmonary hypertension

Respir Med. 2014 Jul;108(7):943-54. doi: 10.1016/j.rmed.2014.04.004. Epub 2014 Apr 29.

Authors

Boris I Medarov¹, Amit Chopra¹, Marc A Judson²

Affiliations

¹ Division of Pulmonary and Critical Care Medicine, Albany Medical College, MC-91, 47 New Scotland Avenue, Albany, NY 12208, USA.
² Division of Pulmonary and Critical Care Medicine, Albany Medical College, MC-91, 47 New Scotland Avenue, Albany, NY 12208, USA. Electronic address: [email protected].

PMID: 24816204
DOI: 10.1016/j.rmed.2014.04.004

Abstract

Portopulmonary hypertension (PoPH) is an often neglected form of pulmonary hypertension where pulmonary hypertension occurs in the presence of portal hypertension. PoPH is important to diagnose and treat as it may improve the patient's quality of life and improve the outcome after liver transplantation. In this review, we discuss the clinical aspects of PoPH including its pathophysiology, diagnosis, treatment, and prognosis.

Keywords: PAH; PoPH; Portopulmonary hypertension.

Publication types

Review

MeSH terms

Genetic Predisposition to Disease
Humans
Hypertension, Portal / diagnosis*
Hypertension, Portal / etiology
Hypertension, Portal / physiopathology
Hypertension, Portal / therapy*
Hypertension, Pulmonary / diagnosis*
Hypertension, Pulmonary / etiology
Hypertension, Pulmonary / physiopathology
Hypertension, Pulmonary / therapy*
Liver Transplantation
Prognosis
Vasodilator Agents / therapeutic use

Substances

Vasodilator Agents