Management of idiopathic pulmonary fibrosis: selected case reports

Eur Respir Rev. 2014 Jun;23(132):239-48. doi: 10.1183/09059180.00002014.

Abstract

In 2011, revised international guidelines were issued jointly by the American Thoracic Society, the European Respiratory Society, the Japanese Respiratory Society and the Latin American Thoracic Association, which provide a valuable framework for the diagnosis and management of idiopathic pulmonary fibrosis (IPF). However, due to the complexity of IPF, these guidelines may not comprehensively account for the management of individual IPF patients in clinical practice. We describe three patient cases that were presented and discussed during the 2013 AIR: Advancing IPF Research meeting in Nice, France. These cases highlight the heterogeneity in the presentation, history and clinical course of IPF, together with expert insights regarding the diagnosis and management of IPF in the real-life setting.

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Aged
  • Anti-Inflammatory Agents / therapeutic use*
  • Disease Progression
  • Fatal Outcome
  • Female
  • Humans
  • Idiopathic Pulmonary Fibrosis / diagnosis
  • Idiopathic Pulmonary Fibrosis / drug therapy*
  • Idiopathic Pulmonary Fibrosis / etiology
  • Idiopathic Pulmonary Fibrosis / physiopathology
  • Lung / diagnostic imaging
  • Lung / drug effects*
  • Lung / physiopathology
  • Male
  • Middle Aged
  • Predictive Value of Tests
  • Pyridones / therapeutic use*
  • Recovery of Function
  • Respiratory Function Tests
  • Risk Factors
  • Smoking / adverse effects
  • Smoking Cessation
  • Time Factors
  • Tomography, X-Ray Computed
  • Treatment Outcome

Substances

  • Anti-Inflammatory Agents
  • Pyridones
  • pirfenidone