Intracardiac mass as initial cardiac manifestation of Behçet's disease: think before you cut

Echocardiography. 2014 Sep;31(8):E243-6. doi: 10.1111/echo.12653. Epub 2014 Jun 13.

Abstract

Behçet's disease (BD) is a chronic multisystemic inflammatory disorder. Cardiac abnormalities including intracardiac thrombi have been described in up to 16% of cases. The clinical presentation of cardiac complications in BD may include fever, dyspnea, chest pain, hemoptysis, and edema. We present 2 cases of patients who underwent surgical excision of intracardiac masses thought to be intracardiac malignancies. Further pathological and clinical evaluation established intracardiac inflammatory masses due to BD as the final diagnosis. As intracardiac masses may be the presenting manifestation of BD, it is crucial for echocardiographers to consider BD in the differential diagnosis. A careful history and physical exam looking for signs and symptoms of BD is critical before considering surgical excision of unexplained intracardiac masses. If the final diagnosis is BD anti-inflammatory therapy should be considered the basis of treatment.

Keywords: Behçet's disease; echocardiography; intracardiac thrombus.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Behcet Syndrome / complications
  • Behcet Syndrome / diagnostic imaging*
  • Behcet Syndrome / surgery*
  • Child
  • Diagnosis, Differential
  • Echocardiography / methods
  • False Positive Reactions
  • Heart Neoplasms / diagnostic imaging*
  • Heart Neoplasms / surgery*
  • Heart Ventricles / diagnostic imaging
  • Heart Ventricles / surgery
  • Humans
  • Male
  • Myocarditis / diagnostic imaging*
  • Myocarditis / etiology
  • Myocarditis / surgery*
  • Preoperative Care / methods
  • Treatment Outcome