Clinical and pathological associations of the activating RAC1 P29S mutation in primary cutaneous melanoma

Pigment Cell Melanoma Res. 2014 Nov;27(6):1117-25. doi: 10.1111/pcmr.12295. Epub 2014 Aug 4.

Abstract

Activating mutations in the GTPase RAC1 are a recurrent event in cutaneous melanoma. We investigated the clinical and pathological associations of RAC1(P29S) in a cohort of 814 primary cutaneous melanomas with known BRAF and NRAS mutation status. The RAC1(P29S) mutation had a prevalence of 3.3% and was associated with increased thickness (OR=1.6 P = 0.001), increased mitotic rate (OR=1.3 P = 0.03), ulceration (OR=2.4 P = 0.04), nodular subtype (OR=3.4 P = 0.004), and nodal disease at diagnosis (OR=3.3 P = 0.006). BRAF mutant tumors were also associated with nodal metastases (OR=1.9 P = 0.004), despite being thinner at diagnosis than BRAF WT (median 1.2 mm versus 1.6 mm, P < 0.001). Immunohistochemical analysis of 51 melanomas revealed that 47% were immunoreactive for RAC1. Melanomas were more likely to show RAC1 immunoreactivity if they were BRAF mutant (OR=5.2 P = 0.01). RAC1 may therefore be important in regulating the early migration of BRAF mutant tumors. RAC1 mutations are infrequent in primary melanomas but may accelerate disease progression.

Keywords: BRAF; RAC1 expression; RAC1 immunoreactivity; RAC1 mutation; melanoma metastasis; melanoma progression.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Aged
  • Amino Acid Substitution*
  • Female
  • GTP Phosphohydrolases / genetics
  • Genetic Association Studies*
  • Genetic Predisposition to Disease*
  • Humans
  • Logistic Models
  • Lymph Nodes / pathology
  • Male
  • Melanoma / genetics*
  • Melanoma / pathology*
  • Membrane Proteins / genetics
  • Middle Aged
  • Multivariate Analysis
  • Mutation / genetics*
  • Proto-Oncogene Proteins B-raf / genetics
  • Ultraviolet Rays
  • rac1 GTP-Binding Protein / genetics*

Substances

  • Membrane Proteins
  • RAC1 protein, human
  • BRAF protein, human
  • Proto-Oncogene Proteins B-raf
  • GTP Phosphohydrolases
  • NRAS protein, human
  • rac1 GTP-Binding Protein