Characteristics and Prognostic Analysis of 69 Patients With Pulmonary Sarcomatoid Carcinoma

Am J Clin Oncol. 2016 Jun;39(3):215-22. doi: 10.1097/COC.0000000000000101.

Abstract

Background: Pulmonary sarcomatoid carcinoma (PSC) is a rare malignancy.

Methods: A total of 69 patients with PSC treated at a single institution in southern China with long-term follow-up were evaluated in this study. We analyzed the clinical characteristics, immunohistochemical profiles, epidermal growth factor receptor mutation status, K-RAS mutation status, treatments, and prognosis.

Results: PSC mainly occurred in young male patients with a history of smoking. Most patients received multimodality treatments and the majority had early-stage disease. The median survival time was 19.1 months, and the 5-year survival rate was 17.4%. The patients without distant metastasis, with normal or higher body mass index (≥18.5), with normal hemoglobin, with smaller tumor size (≤4 cm), and those who received complete resection had significantly better overall survival (P<0.05). The patients with pleomorphic carcinoma had much worse prognosis. In a Cox regression model, M stage, pathology, and having received a complete resection were independent prognostic factors (P<0.05).

Conclusions: PSC is a unique lung malignancy with poor prognosis. Patients receiving complete resection had better prognosis, likely a reflection of early-stage disease. Neither neoadjuvant nor adjuvant chemotherapy improved patient survival for those with early-stage disease. The retrospective design and small sample size limited the generalizability. Future multicenter collaborations may be necessary to determine the optimal treatment.

MeSH terms

  • Adolescent
  • Adult
  • Aged
  • Aged, 80 and over
  • Carcinoma / chemistry
  • Carcinoma / pathology*
  • Carcinoma / secondary
  • Carcinoma / therapy*
  • Carcinoma, Giant Cell / chemistry
  • Carcinoma, Giant Cell / secondary
  • Carcinoma, Giant Cell / therapy
  • Carcinosarcoma / chemistry
  • Carcinosarcoma / secondary
  • Carcinosarcoma / therapy*
  • Combined Modality Therapy
  • Disease-Free Survival
  • ErbB Receptors / genetics
  • Female
  • Follow-Up Studies
  • Humans
  • Keratins / analysis
  • Lung Neoplasms / chemistry
  • Lung Neoplasms / pathology*
  • Lung Neoplasms / therapy*
  • Male
  • Middle Aged
  • Mucin-1 / analysis
  • Nuclear Proteins / analysis
  • Prognosis
  • Proto-Oncogene Proteins p21(ras) / genetics
  • Pulmonary Blastoma / chemistry
  • Pulmonary Blastoma / secondary
  • Pulmonary Blastoma / therapy*
  • S100 Proteins / analysis
  • Survival Rate
  • Thyroid Nuclear Factor 1
  • Transcription Factors / analysis
  • Vimentin / analysis
  • Young Adult

Substances

  • KRAS protein, human
  • Mucin-1
  • Nuclear Proteins
  • S100 Proteins
  • Thyroid Nuclear Factor 1
  • Transcription Factors
  • Vimentin
  • Keratins
  • EGFR protein, human
  • ErbB Receptors
  • Proto-Oncogene Proteins p21(ras)