Human plasmacytoid dendritic cells regulate IFN-α production through activation-induced splicing of IL-18Rα

J Leukoc Biol. 2014 Dec;96(6):1037-46. doi: 10.1189/jlb.2A0813-465RR. Epub 2014 Aug 28.

Abstract

IFN-α production by pDCs regulates host protection against viruses and is implicated in autoimmune pathology. Human pDCs express high levels of IL-18R, but little is known of its role in pDC function. We report that IL-18R signaling negatively regulates IFN-α production through activation-induced splicing of IL-18Rα in human pDCs. Our data reveal two distinct isoforms of IL-18Rα in human pDCs: the known, full-length receptor (IL-18Rα1) and a novel, truncated variant (IL-18Rα2), which functions as a molecular decoy that competitively inhibits the canonical IL-18Rα1/IL-18Rβ signaling pathway. Whereas NK cells and pDCs both express IL-18Rα1, pDCs express significantly higher levels of IL-18Rα2, resulting in differential responses of these populations to IL-18. Flu exposure increases IL-18Rα1 expression in pDCs, and the blocking of IL-18R enhances pDC production of IFN-α and IP-10; thus, pDCs use activation-induced splicing to regulate IFN-α production in response to flu. These data demonstrate that IL-18R modulates IFN-α release by human pDCs and suggest that IL-18R signaling may represent a promising therapeutic target.

Keywords: anti-viral response; inflammation; innate immunity.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Base Sequence
  • Binding, Competitive
  • Cell Differentiation
  • Cells, Cultured
  • Chemokine CXCL10 / biosynthesis
  • Chemokine CXCL10 / genetics
  • Dendritic Cells / metabolism*
  • Gene Expression Regulation / drug effects
  • Gene Expression Regulation / immunology*
  • HEK293 Cells
  • Humans
  • Influenza A Virus, H1N1 Subtype / immunology
  • Interferon-alpha / biosynthesis*
  • Interferon-alpha / genetics
  • Interferon-gamma / biosynthesis
  • Interleukin-12 / pharmacology
  • Interleukin-18 / pharmacology
  • Killer Cells, Natural / cytology
  • Killer Cells, Natural / drug effects
  • Molecular Sequence Data
  • Protein Isoforms / biosynthesis
  • Protein Isoforms / genetics
  • Protein Isoforms / immunology
  • Protein Structure, Tertiary
  • RNA Splicing*
  • Receptors, Interleukin-18 / antagonists & inhibitors
  • Receptors, Interleukin-18 / biosynthesis
  • Receptors, Interleukin-18 / genetics*
  • Receptors, Interleukin-18 / immunology
  • Sequence Alignment
  • Sequence Homology, Nucleic Acid
  • Signal Transduction

Substances

  • CXCL10 protein, human
  • Chemokine CXCL10
  • Interferon-alpha
  • Interleukin-18
  • Protein Isoforms
  • Receptors, Interleukin-18
  • Interleukin-12
  • Interferon-gamma