Upper respiratory system involvement as the only manifestation of granulomatosis with polyangiitis in a child with marfan phenotype

Reza Amin; Soheila Alyasin; Tooba Momen; Maryam Khoshkhouy; Sepideh Darougar

Upper respiratory system involvement as the only manifestation of granulomatosis with polyangiitis in a child with marfan phenotype

Tanaffos. 2013;12(1):74-7.

Authors

Reza Amin¹, Soheila Alyasin¹, Tooba Momen¹, Maryam Khoshkhouy¹, Sepideh Darougar¹

Affiliation

¹ Department of Allergy and Clinical Immunology, Namazi Hospital, Shiraz University of Medical Sciences, Shiraz, Iran.

PMID: 25191453
PMCID: PMC4153231

Abstract

We report a 9-year old girl with an unusual presentation of granulomatosis with polyangiitis in association with Marfan phenotype. The patient presented with recurrent sinusitis, epistaxis, hearing loss and hyperplastic gingivitis, without any signs or symptoms of major organ involvement.

Keywords: Epistaxis; Granulomatosis with Polyangiitis; Hyperplastic gingivitis; Marfan Syndrome; Sinusitis.

Publication types

Case Reports