Conversion from clinically isolated syndrome to multiple sclerosis: A large multicentre study

Mult Scler. 2015 Jul;21(8):1013-24. doi: 10.1177/1352458514568827. Epub 2015 Feb 13.

Abstract

Background and objective: We explored which clinical and biochemical variables predict conversion from clinically isolated syndrome (CIS) to clinically definite multiple sclerosis (CDMS) in a large international cohort.

Methods: Thirty-three centres provided serum samples from 1047 CIS cases with at least two years' follow-up. Age, sex, clinical presentation, T2-hyperintense lesions, cerebrospinal fluid (CSF) oligoclonal bands (OCBs), CSF IgG index, CSF cell count, serum 25-hydroxyvitamin D3 (25-OH-D), cotinine and IgG titres against Epstein-Barr nuclear antigen 1 (EBNA-1) and cytomegalovirus were tested for association with risk of CDMS.

Results: At median follow-up of 4.31 years, 623 CIS cases converted to CDMS. Predictors of conversion in multivariable analyses were OCB (HR = 2.18, 95% CI = 1.71-2.77, p < 0.001), number of T2 lesions (two to nine lesions vs 0/1 lesions: HR = 1.97, 95% CI = 1.52-2.55, p < 0.001; >9 lesions vs 0/1 lesions: HR = 2.74, 95% CI = 2.04-3.68, p < 0.001) and age at CIS (HR per year inversely increase = 0.98, 95% CI = 0.98-0.99, p < 0.001). Lower 25-OH-D levels were associated with CDMS in univariable analysis, but this was attenuated in the multivariable model. OCB positivity was associated with higher EBNA-1 IgG titres.

Conclusions: We validated MRI lesion load, OCB and age at CIS as the strongest independent predictors of conversion to CDMS in this multicentre setting. A role for vitamin D is suggested but requires further investigation.

Keywords: Clinically definite multiple sclerosis (CDMS); Epstein-Barr nuclear antigen 1 (EBNA-1); clinically isolated syndrome (CIS); oligoclonal bands (OCBs); serum 25-hydroxyvitamin D3 (25-OH-D).

Publication types

  • Multicenter Study
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adult
  • Cohort Studies
  • Disease Progression
  • Endonucleases
  • Female
  • Follow-Up Studies
  • Humans
  • Immunoglobulin G / analysis
  • Magnetic Resonance Imaging
  • Male
  • Multiple Sclerosis / cerebrospinal fluid
  • Multiple Sclerosis / pathology*
  • Nuclear Proteins / analysis
  • Oligoclonal Bands / genetics
  • Predictive Value of Tests
  • Prognosis
  • Risk Assessment
  • Survival Analysis
  • Vitamin D / blood

Substances

  • Immunoglobulin G
  • Nuclear Proteins
  • Oligoclonal Bands
  • Vitamin D
  • Endonucleases
  • SND1 protein, human