Eculizumab in pregnancy-associated atypical hemolytic uremic syndrome: insights for optimizing management

J Nephrol. 2015 Oct;28(5):641-5. doi: 10.1007/s40620-015-0173-5. Epub 2015 Feb 25.

Abstract

Pregnancy-associated atypical hemolytic uremic syndrome is a systemic disease associated with high morbidity and mortality rates, caused by dysregulation of the alternative complement pathway, leading to uncontrolled complement activation resulting in thrombotic microangiopathy. This condition can be effectively treated by anti-C5 therapy, which controls complement activation. Treatment can be safely discontinued after complete remission and resolution of the precipitating cause, especially in patients with a low-risk genetic profile.

Keywords: Eculizumab; Hemolytic uremic syndrome; Post-partum; Pregnancy.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Antibodies, Monoclonal, Humanized / administration & dosage*
  • Atypical Hemolytic Uremic Syndrome / diagnosis
  • Atypical Hemolytic Uremic Syndrome / drug therapy*
  • Biopsy
  • Diagnosis, Differential
  • Disease Management*
  • Female
  • Follow-Up Studies
  • Humans
  • Kidney / pathology
  • Pregnancy
  • Pregnancy Complications / drug therapy*
  • Remission Induction

Substances

  • Antibodies, Monoclonal, Humanized
  • eculizumab