[Tumor cytogenetics and prognosis in neuroblastoma]

Monatsschr Kinderheilkd. 1989 Oct;137(10):666-71.
[Article in German]

Abstract

In 40 children with neuroblastoma of different clinical stages the tumorkaryotype was determined at onset (n = 30) or at relapse (n = 10) of disease after short-term culture of tumor tissues or bone marrow aspirates. None of the 10 stage I, II, and IVs tumors revealed a chromosome 1p aberration, in contrast to stage III and IV tumors where this abnormality was encountered in 25 (=83%) of 30 patients. Amplification of the proto-oncogene N-myc in the tumor-DNA could not be detected in stage I, II and IVs, was however present in 53% of stage III and IV tumors. Cytogenetic phenomena of gene amplification such as Double minutes (DMs) and Homogeneously Staining Regions (HSRs) correlated with N-myc amplification. About 50% of stage III and IV tumors had chromosome numbers in the neardiploid range whereas prognostically favourable tumors were characterized by hyperploid chromosomal numbers mainly in the triploid range. Life-table analysis according to Kaplan-Meier showed a probability of surviving in about 80% of patients with a normal morphology of chromosome 1 in their tumor cells, compared to about 60% in the absence of N-myc oncogene amplification and of about 50%, if aneuploidy is detected. Thus, we think, the presence or absence of chromosome 1p aberration in the tumorkaryotype is the most sensitive discriminator for outcome in children with neuroblastoma.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Aneuploidy
  • Child
  • Child, Preschool
  • Chromosome Aberrations*
  • Chromosomes, Human, Pair 1*
  • DNA Probes
  • DNA, Neoplasm / genetics*
  • Female
  • Gene Amplification
  • Humans
  • Infant
  • Karyotyping*
  • Male
  • Neoplasm Recurrence, Local / genetics
  • Neuroblastoma / genetics*
  • Neuroblastoma / pathology
  • Oncogenes
  • Prognosis
  • Proto-Oncogene Mas

Substances

  • DNA Probes
  • DNA, Neoplasm
  • MAS1 protein, human
  • Proto-Oncogene Mas