Perfusion and pH MRI in familial hemiplegic migraine with prolonged aura

Cephalalgia. 2016 Mar;36(3):279-83. doi: 10.1177/0333102415586064. Epub 2015 May 6.

Abstract

Introduction: To investigate tissue flow disturbance and hypoxia during migraine aura, we studied a case of familial hemiplegic migraine (FHM) using novel magnetic resonance imaging (MRI) techniques.

Case results: A 44-year-old male was admitted with suspected stroke because of confusion and aphasia. Initial gadolinium-based perfusion MRI showed a decrease in cerebral blood flow and an increase in capillary flow disturbances within the left hemisphere. Later during the prolonged aura phase, chemical exchange saturation transfer MRI indicated a drop in pH in the affected area. The patient was diagnosed with an R908Q mutation in the ATP1A2 gene causing FHM type 2.

Discussion: During prolonged aura in FHM, MRI shows reduced CBF, capillary flow disturbances and a possible pH drop that could indicate tissue hypoxia.

Keywords: MRI; Migraine; cerebral blood flow; chemical exchange saturation transfer; familial hemiplegic migraine; genetics; pH.

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adult
  • Cerebrovascular Circulation / physiology
  • Humans
  • Hydrogen-Ion Concentration
  • Image Interpretation, Computer-Assisted
  • Magnetic Resonance Imaging / methods*
  • Male
  • Migraine with Aura / genetics
  • Migraine with Aura / physiopathology*
  • Mutation
  • Pedigree
  • Sodium-Potassium-Exchanging ATPase / genetics

Substances

  • ATP1A2 protein, human
  • Sodium-Potassium-Exchanging ATPase

Supplementary concepts

  • Hemiplegic migraine, familial type 2