Kikuchi disease, macrophage activation syndrome, and systemic juvenile arthritis: a new case associated with a mutation in the perforin gene

MeSH terms

• Adolescent
• Antirheumatic Agents / therapeutic use
• Arthritis, Juvenile / diagnosis
• Arthritis, Juvenile / drug therapy
• Arthritis, Juvenile / genetics*
• Female
• Histiocytic Necrotizing Lymphadenitis / diagnosis
• Histiocytic Necrotizing Lymphadenitis / drug therapy
• Histiocytic Necrotizing Lymphadenitis / genetics*
• Humans
• Interleukin 1 Receptor Antagonist Protein / therapeutic use
• Macrophage Activation Syndrome / diagnosis
• Macrophage Activation Syndrome / drug therapy
• Macrophage Activation Syndrome / genetics*
• Mutation / genetics*
• Perforin / genetics*
• Syndrome
• Treatment Outcome