Non-aneurysmal abdominal aortic rupture in a patient with Marfan syndrome

Asian Cardiovasc Thorac Ann. 2016 Sep;24(7):703-6. doi: 10.1177/0218492315593225. Epub 2015 Jun 24.

Abstract

Aortic rupture in the presence of aneurysmal disease is well understood and extensively described in the literature. However, aortic rupture in a non-aneurysmal aorta is far less common. In the few reported cases, perforations are believed to result from a penetrating atheromatous ulcer of the aorta. We describe a rare case of non-aneurysmal aortic rupture in a 68-year-old man with Marfan syndrome and a history of proximal aortic surgery. The urgent need for hemorrhage control precluded any consideration of an endovascular repair.

Keywords: Aorta; Aortic aneurysm; Blood vessel prosthesis implantation; Marfan syndrome; abdominal.

Publication types

  • Case Reports

MeSH terms

  • Aged
  • Aortic Rupture / diagnostic imaging
  • Aortic Rupture / etiology*
  • Aortic Rupture / surgery
  • Aortography / methods
  • Blood Vessel Prosthesis Implantation
  • Fatal Outcome
  • Hemorrhage / diagnostic imaging
  • Hemorrhage / etiology*
  • Hemorrhage / surgery
  • Hemostatic Techniques
  • Humans
  • Male
  • Marfan Syndrome / complications*
  • Marfan Syndrome / diagnosis
  • Tomography, X-Ray Computed
  • Treatment Outcome