Pulmonary mucosa-associated lymphoma in a patient with von Hippel-Lindau disease

David M Straughan; Sid Kerkar; Saїd C Azoury; Emily S Reardon; David S Schrump

doi:10.1093/jscr/rjv080

Pulmonary mucosa-associated lymphoma in a patient with von Hippel-Lindau disease

J Surg Case Rep. 2015 Jul 14;2015(7):rjv080. doi: 10.1093/jscr/rjv080.

Authors

David M Straughan¹, Sid Kerkar², Saїd C Azoury³, Emily S Reardon³, David S Schrump³

Affiliations

¹ Department of Thoracic and GI Oncology, National Cancer Institute, National Institutes of Health, Bethesda, MD 20892, USA [email protected].
² Department of Pathology, National Cancer Institute, National Institutes of Health, Bethesda, MD 20892, USA.
³ Department of Thoracic and GI Oncology, National Cancer Institute, National Institutes of Health, Bethesda, MD 20892, USA.

Abstract

A 61-year-old female with a past medical history significant for von Hippel-Lindau (VHL) syndrome presented with multiple bilateral pulmonary lesions found on surveillance computed tomography scan. Positron emission tomography demonstrated avidity in a lesion in the right upper lobe. After an equivocal biopsy, a lobectomy via a thoracoscopic approach was performed as this lesion was concerning for a primary lung cancer. Pathology revealed a diagnosis of pulmonary mucosa-associated lymphoid tissue (MALT) lymphoma. To our knowledge, this is the first reported case of a pulmonary MALT lymphoma in a patient with VHL.

Publication types

Case Reports