A novel mutation in the TMC1 gene causes non-syndromic hearing loss in a Moroccan family

Gene. 2015 Dec 10;574(1):28-33. doi: 10.1016/j.gene.2015.07.075. Epub 2015 Jul 28.

Abstract

Autosomal recessive non-syndromic hearing loss (ARNSHL) is one of the most common genetic diseases in human and is subject to important genetic heterogeneity, rendering molecular diagnosis difficult. Whole-exome sequencing is thus a powerful strategy for this purpose. After excluding GJB2 mutation and other common mutations associated with hearing loss in Morocco, whole-exome sequencing was performed to study the genetic causes of one sibling with ARSHNL in a consanguineous Moroccan family. After filtering data and Sanger sequencing validation, one novel pathogenic homozygous mutation c.1810C>G (p.Arg604Gly) was identified in TMC1, a gene reported to cause deafness in various populations. Thus, we identified here the first mutation in the TMC1 gene in the Moroccan population causing non-syndromic hearing loss.

Keywords: Hearing loss; Morocco; Mutation; TMC1; Whole exome sequencing.

MeSH terms

  • Connexin 26
  • Connexins
  • Deafness / genetics
  • Exome / genetics
  • Female
  • Genes, Recessive / genetics
  • Hearing Loss / genetics*
  • Homozygote
  • Humans
  • Male
  • Membrane Proteins / genetics*
  • Morocco
  • Mutation / genetics*
  • Pedigree

Substances

  • Connexins
  • GJB2 protein, human
  • Membrane Proteins
  • TMC1 protein, human
  • Connexin 26