Prenatal diagnosis and follow-up of a case of branchio-oto-renal syndrome displays renal growth impairment after the second trimester

J Obstet Gynaecol Res. 2015 Nov;41(11):1831-4. doi: 10.1111/jog.12791. Epub 2015 Jul 30.

Abstract

Branchio-oto-renal syndrome combines branchial arch defects, hearing impairment and renal malformations or hypoplasia. Due to the high phenotypic variability, prenatal diagnosis has a limited prognostic value in mutation-positive cases. We report the first branchio-oto-renal syndrome molecular prenatal diagnosis and ultrasonographic follow-up, showing a normal renal growth until the 24th week of pregnancy, a growth deceleration during the third trimester and a renal volume recovery during the first months of life.

Keywords: branchio-oto-renal syndrome; genetic test; prenatal diagnosis.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adult
  • Branchio-Oto-Renal Syndrome / diagnosis*
  • Branchio-Oto-Renal Syndrome / genetics
  • Female
  • Follow-Up Studies
  • Humans
  • Kidney / embryology*
  • Molecular Diagnostic Techniques*
  • Mutation*
  • Pregnancy
  • Pregnancy Trimester, Second
  • Prenatal Diagnosis / methods*
  • Ultrasonography, Prenatal