Postencephalitic epilepsy and drug-resistant epilepsy after infectious and antibody-associated encephalitis in childhood: Clinical and etiologic risk factors

Epilepsia. 2016 Jan;57(1):e7-e11. doi: 10.1111/epi.13253. Epub 2015 Nov 22.

Abstract

To define the risk factors for postencephalitic epilepsy (PE) and drug-resistant epilepsy (DRE) in childhood following infectious and autoimmune encephalitis, we included 147 acute encephalitis patients with a median follow-up of 7.3 years (range 2-15.8 years). PE was defined as the use of antiepileptic drugs (AEDs) for ≥24 months, and DRE was defined as the persistence of seizures despite ≥2 appropriate AEDs at final follow-up. PE and DRE were diagnosed in 31 (21%) and 15 (10%) of patients, respectively. The features during acute encephalitis predictive of DRE (presented as odds ratio [OR] with confidence intervals [CIs]) were status epilepticus (OR 10.8, CI 3.4-34.3), visual disturbance (6.4, 1.4-29.9), focal seizures (6.2, 1.9-20.6), magnetic resonance imaging (MRI) hippocampal/amygdala involvement (5.0, 1.7-15.4), intensive care admission (4.7, 1.4-15.4), use of >3 AEDs (4.5, 1.2-16.1), MRI gadolinium enhancement (4.1, 1.2-14.2), any seizure (3.9, 1.1-14.4), and electroencephalography (EEG) epileptiform discharges (3.9, 1.3-12.0). On multivariable regression analysis, only status epilepticus remained predictive of DRE in all models. DRE was common in herpes simplex virus (3/9, 33%) and unknown (8/40, 20%) encephalitis, but absent in acute disseminated encephalomyelitis (ADEM) (0/32, 0%), enterovirus (0/18), and anti-N-methyl-d-aspartate receptor-NMDAR encephalitis (0/9). We have identified risk factors for DRE and demonstrated "high-risk," and "low-risk" etiologies.

Keywords: Autoimmune; Encephalitis; Epilepsy; Infection; Outcome.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adolescent
  • Autoantibodies / blood
  • Child
  • Child, Preschool
  • Cohort Studies
  • Drug Resistant Epilepsy / etiology*
  • Electroencephalography
  • Encephalitis / complications*
  • Encephalitis / immunology*
  • Epilepsy / blood
  • Epilepsy / etiology*
  • Female
  • Glutamate Decarboxylase / immunology
  • Humans
  • Male
  • Membrane Proteins / immunology
  • Nerve Tissue Proteins / immunology
  • Potassium Channels, Voltage-Gated / immunology
  • ROC Curve
  • Receptors, N-Methyl-D-Aspartate / immunology*
  • Risk Factors

Substances

  • Autoantibodies
  • CNTNAP2 protein, human
  • Membrane Proteins
  • Nerve Tissue Proteins
  • Potassium Channels, Voltage-Gated
  • Receptors, N-Methyl-D-Aspartate
  • Glutamate Decarboxylase