[Detection of subtelomeric copy number variations in children with intellectual disability]

Zhongguo Dang Dai Er Ke Za Zhi. 2015 Dec;17(12):1273-6.
[Article in Chinese]

Abstract

Objective: To detect subtelomeric copy number variations in children with genetic intellectual disability (ID) using multiplex ligation-dependent probe amplification (MLPA), and to investigate the pathogenesis of genetic ID.

Methods: A total of 68 children with ID who had normal results of G-banding karyotype analysis were included in the study. Their subtelomeric copy number variations were detected using MLPA P036.

Results: Among the 68 children with ID, 7(10%) showed subtelomeric copy number variations, and all the variations were deletion mutations. Among them, 1 case carried 2 subtelomeric microdeletions, and 1 case carried 4 subtelomeric microdeletions.

Conclusions: Subtelomeric copy number variations are important causes of genetic ID. MLPA can be used as an economic and effective method for investigating the pathogenesis of genetic ID.

Publication types

  • English Abstract

MeSH terms

  • Adolescent
  • Child
  • Child, Preschool
  • DNA Copy Number Variations*
  • Female
  • Humans
  • Infant
  • Intellectual Disability / genetics*
  • Male
  • Multiplex Polymerase Chain Reaction
  • Telomere*