Prenatal Features of Bladder Agenesis in a Female Fetus with Genital Transposition

Fetal Pediatr Pathol. 2016;35(1):37-42. doi: 10.3109/15513815.2015.1122122. Epub 2015 Dec 31.

Abstract

Bladder agenesis is a rare condition, mostly affecting females, where diagnosis is usually made in infancy when investigating urinary incontinence. Neonatal cases are uncommon, and none have been reported antenatally. The few male patients with this condition rarely survive: among associated anomalies, different degrees of penoscrotal transposition are the most evident feature. The association of genital transposition in a female infant with prenatal description of bladder agenesis has not been previously reported. Early diagnosis is important, enabling planning of surgical reconstruction early in life and appropriate parental counseling.

Keywords: bladder agenesis; genital transposition; prenatal diagnosis; urinary incontinence.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Female
  • Genital Diseases, Female / diagnosis
  • Genital Diseases, Female / pathology*
  • Genital Diseases, Female / surgery
  • Humans
  • Infant
  • Pregnancy
  • Prenatal Diagnosis
  • Treatment Outcome
  • Urinary Bladder Diseases / diagnosis
  • Urinary Bladder Diseases / pathology*
  • Urinary Bladder Diseases / surgery