Loss of ezrin in human intrahepatic cholangiocarcinoma is associated with ectopic expression of E-cadherin

Histopathology. 2016 Aug;69(2):211-21. doi: 10.1111/his.12931. Epub 2016 Mar 1.

Abstract

Aims: Ezrin connects proteins from the plasma membrane to the subcortical cytoskeleton, and contributes to epithelial integrity by interacting with the cell-cell adhesion molecule E-cadherin. In the liver, ezrin is restricted to cholangiocytes, where it regulates biliary secretory functions. During carcinogenesis, ezrin expression is impaired and associated with enhancement of cell migratory activity in cancer cells; therefore, we aimed to analyse ezrin in cholangiocarcinogenesis.

Methods and results: Ezrin expression was evaluated by immunohistochemistry on tissue microarrays from 94 surgical specimens of intrahepatic cholangiocarcinoma (CCA), and correlated with clinicopathological factors and E-cadherin expression. Ezrin function was also analysed in human CCA cell lines. In CCA, ezrin was negative/weakly expressed in 49 cases (52%) and moderately/strongly expressed in 45 cases (48%), mostly in cell cytoplasm. The negative/weak expression of ezrin was more frequent in peripheral than in perihilar CCA (P = 0.002), and was associated with high tumour size (P = 0.001), low mucus secretion (P = 0.042), the presence of satellite nodules (P = 0.024), and ectopic cytoplasmic expression of E-cadherin (P = 0.005). In vitro, silencing of ezrin in CCA cells caused internalization of E-cadherin and favoured cell migration.

Conclusions: Ezrin is down-regulated during cholangiocarcinogenesis, and its loss results in a more aggressive phenotype.

Keywords: E-cadherin; cellular biology; cholangiocarcinoma; ezrin; immunohistochemistry.

MeSH terms

  • Aged
  • Antigens, CD
  • Bile Duct Neoplasms / diagnosis
  • Bile Duct Neoplasms / metabolism*
  • Bile Duct Neoplasms / pathology
  • Bile Duct Neoplasms / surgery
  • Biomarkers, Tumor / metabolism*
  • Cadherins / metabolism*
  • Carcinogenesis
  • Cell Line, Tumor
  • Cell Membrane / metabolism
  • Cell Movement
  • Cholangiocarcinoma / diagnosis
  • Cholangiocarcinoma / metabolism*
  • Cholangiocarcinoma / pathology
  • Cholangiocarcinoma / surgery
  • Cytoskeletal Proteins / metabolism*
  • Down-Regulation
  • Ectopic Gene Expression
  • Gene Expression Regulation, Neoplastic
  • Humans
  • Immunohistochemistry
  • Liver / metabolism
  • Liver / pathology
  • Liver Neoplasms / diagnosis
  • Liver Neoplasms / metabolism*
  • Liver Neoplasms / pathology
  • Liver Neoplasms / surgery
  • Tissue Array Analysis

Substances

  • Antigens, CD
  • Biomarkers, Tumor
  • CDH1 protein, human
  • Cadherins
  • Cytoskeletal Proteins
  • ezrin