The mitochondrial Ca2+ uniporter: regulation by auxiliary subunits and signal transduction pathways

Am J Physiol Cell Physiol. 2016 Jul 1;311(1):C67-80. doi: 10.1152/ajpcell.00319.2015. Epub 2016 Apr 27.

Abstract

Mitochondrial Ca(2+) homeostasis, the Ca(2+) influx-efflux balance, is responsible for the control of numerous cellular functions, including energy metabolism, generation of reactive oxygen species, spatiotemporal dynamics of Ca(2+) signaling, and cell growth and death. Recent discovery of the molecular identity of the mitochondrial Ca(2+) uniporter (MCU) provides new possibilities for application of genetic approaches to study the mitochondrial Ca(2+) influx mechanism in various cell types and tissues. In addition, the subsequent discovery of various auxiliary subunits associated with MCU suggests that mitochondrial Ca(2+) uptake is not solely regulated by a single protein (MCU), but likely by a macromolecular protein complex, referred to as the MCU-protein complex (mtCUC). Moreover, recent reports have shown the potential role of MCU posttranslational modifications in the regulation of mitochondrial Ca(2+) uptake through mtCUC. These observations indicate that mtCUCs form a local signaling complex at the inner mitochondrial membrane that could significantly regulate mitochondrial Ca(2+) handling, as well as numerous mitochondrial and cellular functions. In this review we discuss the current literature on mitochondrial Ca(2+) uptake mechanisms, with a particular focus on the structure and function of mtCUC, as well as its regulation by signal transduction pathways, highlighting current controversies and discrepancies.

Keywords: CCDC109A; Ca2+/calmodulin-dependent protein kinase II; MCUb; phosphorylation; proline-rich tyrosine kinase 2.

Publication types

  • Review
  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Calcium Channels / chemistry
  • Calcium Channels / genetics
  • Calcium Channels / metabolism*
  • Calcium Signaling*
  • Calcium-Calmodulin-Dependent Protein Kinase Type 2 / metabolism
  • Homeostasis
  • Humans
  • Ion Channel Gating
  • Mitochondria / metabolism*
  • Mitochondrial Membranes / metabolism*
  • Phosphorylation
  • Protein Processing, Post-Translational
  • Protein Structure, Quaternary
  • Protein Subunits
  • RNA Processing, Post-Transcriptional
  • Structure-Activity Relationship
  • Transcription, Genetic

Substances

  • Calcium Channels
  • Protein Subunits
  • mitochondrial calcium uniporter
  • Calcium-Calmodulin-Dependent Protein Kinase Type 2