Sclerosing mesenteric panniculitis in a young patient : common cause of diagnostic dilemma and treatment refractoriness

Acta Gastroenterol Belg. 2016 Apr-Jun;79(2):254-6.

Abstract

Background: Sclerosing mesenteric panniculitis (SMP) is an idiopathic chronic fibroinflammatory disorder of the intra-abdominal fat.

Case presentation: Herin, we report a case of SMP, involving the omentum, mesentery and peri-colic fat in a 18 year old male, who presented with significant and recurrent abdominal distension for 4.5 years. Computed tomogram revealed ascites, with nodular and irregular omental thickening and foci of calcification. Non-specific radiological and histological features made an accurate diagnosis extremely difficult. After a thorough work up and exclusion of other differentials, diagnosis of a nodular SMP (Weber Christian disease) was given. After showing resistance to chemotherapeutic agents, slow response was noted with cyclophosphamide, followed by rapid symptomatic improvement with mesenterectomy.

Conclusion: SMP is an uncommon benign mesenteric/ omental inflammation, and is a diagnosis of exclusion. As treatment refractoriness is common, management should be individualized and continued for along period. Surgical omentectomy may be helpful.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Biopsy
  • Humans
  • Immunosuppressive Agents / therapeutic use
  • Male
  • Mesentery / diagnostic imaging
  • Mesentery / pathology*
  • Mesentery / surgery
  • Omentum / diagnostic imaging
  • Omentum / pathology*
  • Omentum / surgery
  • Panniculitis, Peritoneal / diagnosis*
  • Panniculitis, Peritoneal / therapy
  • Tomography, X-Ray Computed

Substances

  • Immunosuppressive Agents