Skeletal muscle fiber-type specific succinate dehydrogenase activity in cerebral palsy

Muscle Nerve. 2017 Jan;55(1):122-124. doi: 10.1002/mus.25379. Epub 2016 Sep 26.

Abstract

Introduction: Children with cerebral palsy (CP) exhibit increased energy expenditure during movement, but whether this is due in part to decrements in skeletal muscle mitochondrial oxidative capacity is unknown. Accordingly, we compared fiber-type specific succinate dehydrogenase (SDH) activity in children with CP with typically developing (TD) children.

Methods: SDH activity and myofiber areas of type 1 and 2A fibers were measured in semitendinosus biopsies of both groups (n = 5/group).

Results: SDH activity was ∼35% higher in type 1 compared with type 2A fibers, but there were no differences between groups. Average myofiber area was 45% smaller in CP versus TD (P < 0.05), and type 2A fibers were 32% larger than type 1 fibers (P < 0.05) only in TD children.

Conclusions: Fiber-type specific SDH activity is similar between TD children and children with CP. This suggests that increased energy expenditure in children with CP is not related to impaired mitochondrial oxidative capacity. Muscle Nerve, 2016 Muscle Nerve 55: 122-124, 2017.

Keywords: cerebral palsy; energy expenditure; fiber type; oxidative capacity; skeletal muscle; succinate dehydrogenase.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, U.S. Gov't, Non-P.H.S.

MeSH terms

  • Adolescent
  • Cerebral Palsy / pathology*
  • Child
  • Female
  • Humans
  • Laminin / metabolism
  • Male
  • Muscle Fibers, Skeletal / enzymology*
  • Succinate Dehydrogenase / metabolism*
  • Young Adult

Substances

  • Laminin
  • Succinate Dehydrogenase