Waking up dormant tumor suppressor genes with zinc fingers, TALEs and the CRISPR/dCas9 system

Oncotarget. 2016 Sep 13;7(37):60535-60554. doi: 10.18632/oncotarget.11142.

Abstract

The aberrant epigenetic silencing of tumor suppressor genes (TSGs) plays a major role during carcinogenesis and regaining these dormant functions by engineering of sequence-specific epigenome editing tools offers a unique opportunity for targeted therapies. However, effectively normalizing the expression and regaining tumor suppressive functions of silenced TSGs by artificial transcription factors (ATFs) still remains a major challenge. Herein we describe novel combinatorial strategies for the potent reactivation of two class II TSGs, MASPIN and REPRIMO, in cell lines with varying epigenetic states, using the CRISPR/dCas9 associated system linked to a panel of effector domains (VP64, p300, VPR and SAM complex), as well as with protein-based ATFs, Zinc Fingers and TALEs. We found that co-delivery of multiple effector domains using a combination of CRISPR/dCas9 and TALEs or SAM complex maximized activation in highly methylated promoters. In particular, CRISPR/dCas9 VPR with SAM upregulated MASPIN mRNA (22,145-fold change) in H157 lung cancer cells, with accompanying re-expression of MASPIN protein, which led to a concomitant inhibition of cell proliferation and induction of apoptotic cell death. Consistently, CRISPR/dCas9 VP64 with SAM upregulated REPRIMO (680-fold change), which led to phenotypic reprogramming in AGS gastric cancer cells. Altogether, our results outlined novel sequence-specific, combinatorial epigenome editing approaches to reactivate highly methylated TSGs as a promising therapy for cancer and other diseases.

Keywords: CRISPR/dCas9; TALE; ZF; gene reactivation; tumor suppressor genes.

MeSH terms

  • Apoptosis
  • CRISPR-Cas Systems / genetics*
  • Cell Cycle Proteins / genetics
  • Cell Cycle Proteins / metabolism
  • Cell Line, Tumor
  • Cell Proliferation
  • DNA Methylation
  • Epigenesis, Genetic
  • Gene Expression Regulation, Neoplastic
  • Glycoproteins / genetics
  • Glycoproteins / metabolism
  • Homeodomain Proteins / genetics*
  • Humans
  • Lung Neoplasms / genetics
  • Lung Neoplasms / metabolism*
  • RNA, Long Noncoding / genetics*
  • Repressor Proteins / genetics*
  • Serpins / genetics
  • Serpins / metabolism
  • Sterile Alpha Motif / genetics*
  • Stomach Neoplasms / genetics
  • Stomach Neoplasms / metabolism*
  • Transcriptional Activation
  • Tumor Suppressor Proteins / genetics
  • Tumor Suppressor Proteins / metabolism
  • Zinc Fingers / genetics*

Substances

  • Cell Cycle Proteins
  • Glycoproteins
  • Homeodomain Proteins
  • RNA, Long Noncoding
  • RPRM protein, human
  • Repressor Proteins
  • SERPIN-B5
  • Serpins
  • TGIF1 protein, human
  • Tumor Suppressor Proteins
  • long noncoding RNA CASC9, human