Radiological and Clinical Features of Eosinophilic Granulomatosis with Polyangiitis

Zhongguo Yi Xue Ke Xue Yuan Xue Bao. 2016 Oct 10;38(5):617-620. doi: 10.3881/j.issn.1000-503X.2016.05.023.

Abstract

Eosinophilic granulomatosis with polyangiitis(EGPA),also known as Churg-Strauss syndrome,is a clinically rare small-vessel vasculitis associated with antineutrophil cytoplasmic antibodies (ANCAs) and the hypereosinophilic syndromes (HESs),characterized by asthma,disseminated necrotizing vasculitis,extravascular granulomas,peripheral eosinophilia,and tissue eosinophilia. This article reviews the pathology,imaging,and clinical features of EGPA.

Publication types

  • Review

MeSH terms

  • Antibodies, Antineutrophil Cytoplasmic
  • Asthma
  • Churg-Strauss Syndrome / diagnosis*
  • Churg-Strauss Syndrome / pathology
  • Eosinophilia
  • Granulomatosis with Polyangiitis / diagnosis*
  • Granulomatosis with Polyangiitis / pathology
  • Humans

Substances

  • Antibodies, Antineutrophil Cytoplasmic