Type B Insulin Resistance Masquerading as Ovarian Hyperthecosis

J Clin Endocrinol Metab. 2017 Jun 1;102(6):1789-1791. doi: 10.1210/jc.2016-3674.

Abstract

Context: Hyperinsulinemia can lead to pathologic ovarian growth and androgen production.

Case description: A 29-year-old woman developed an autoantibody to the insulin receptor (type B insulin resistance), causing extreme insulin resistance and hyperinsulinemia. Testosterone levels were elevated to the adult male range. Treatment with gonadotropin-releasing hormone (GnRH) analog led to normalization of testosterone, despite persistent extreme insulin resistance.

Conclusions: This case demonstrates that gonadotropins are necessary for insulin to cause pathologic ovarian androgen production. Suppression of gonadotropins with GnRH analogs may be a useful therapeutic option in patients with severe hyperandrogenism or ovarian enlargement because of hyperinsulinemia.

Trial registration: ClinicalTrials.gov NCT00001987.

Publication types

  • Case Reports
  • Research Support, N.I.H., Intramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adult
  • Antineoplastic Agents, Hormonal / therapeutic use
  • Autoantibodies / immunology
  • Cyclophosphamide / therapeutic use
  • Dexamethasone / therapeutic use
  • Diagnosis, Differential
  • Female
  • Gonadotropin-Releasing Hormone / analogs & derivatives
  • Humans
  • Hyperandrogenism / blood
  • Hyperandrogenism / diagnosis*
  • Hyperandrogenism / drug therapy
  • Hyperinsulinism / blood
  • Hyperinsulinism / diagnosis*
  • Immunosuppressive Agents / therapeutic use
  • Insulin Resistance / immunology*
  • Leuprolide / therapeutic use
  • Ovarian Diseases / blood
  • Ovarian Diseases / diagnosis*
  • Ovarian Diseases / drug therapy
  • Receptor, Insulin / immunology*
  • Rituximab / therapeutic use
  • Testosterone / blood

Substances

  • Antineoplastic Agents, Hormonal
  • Autoantibodies
  • Immunosuppressive Agents
  • Gonadotropin-Releasing Hormone
  • Testosterone
  • Rituximab
  • Dexamethasone
  • Cyclophosphamide
  • Receptor, Insulin
  • Leuprolide

Associated data

  • ClinicalTrials.gov/NCT00001987