Diagnostic significance of IgG, C3, and C9 at the limb muscle motor end-plate in minimal myasthenia gravis

Neurology. 1989 Oct;39(10):1359-63. doi: 10.1212/wnl.39.10.1359.

Abstract

We detected deposits of IgG, C3, and C9 (immune complexes) at the limb muscle motor end-plates (biceps brachii muscle) in 16 of 19 patients who exhibited only ocular signs and symptoms of myasthenia gravis that were improved by intravenous injections of edrophonium chloride. Circulating anti-acetylcholine receptor (anti-AChR) antibodies were negative in 6 of the 16 patients, but the motor end-plate fine structure in the postsynaptic regions was abnormal in all 16. Single-fiber EMG revealed no abnormalities in 8 of 13 patients studied. Our results indicate that the detection of immune complexes at the limb muscle end-plate provides a highly sensitive and confirmative method for diagnosing patients with minimal or atypical myasthenia gravis who have no detectable anti-AChR antibodies in their serum.

MeSH terms

  • Adolescent
  • Adult
  • Antibodies / analysis
  • Antigen-Antibody Complex / analysis*
  • Child
  • Child, Preschool
  • Complement C3 / analysis*
  • Electromyography
  • Extremities
  • Female
  • Humans
  • Immunoglobulin G / analysis*
  • Male
  • Middle Aged
  • Motor Endplate / analysis*
  • Muscles / innervation
  • Myasthenia Gravis / blood
  • Myasthenia Gravis / diagnosis*
  • Myasthenia Gravis / immunology
  • Neuromuscular Junction / analysis*
  • Receptors, Cholinergic / immunology

Substances

  • Antibodies
  • Antigen-Antibody Complex
  • Complement C3
  • Immunoglobulin G
  • Receptors, Cholinergic