Short segment myelitis as a first manifestation of neuromyelitis optica spectrum disorders

Mult Scler. 2017 Mar;23(3):413-419. doi: 10.1177/1352458516687043. Epub 2017 Jan 9.

Abstract

Background: Some patients with neuromyelitis optica spectrum disorders (NMOSD) present with spinal cord lesions extending fewer than three vertebral segments (short transverse myelitis, STM), hindering an early diagnosis.

Objective: We investigated the frequency and imaging characteristics of STM lesions in patients presenting with myelitis as an initial manifestation of NMOSD.

Methods: Patients seen at three referral hospitals in Korea between June 2005 and March 2015 who met the following inclusion criteria were recruited for review: seropositivity for aquaporin-4 antibody, initial presentation with myelitis and spinal cord magnetic resonance imaging (MRI) performed within 1 month of initial myelitis onset.

Results: Of the 76 enrolled patients, 65 (85.5%) collectively had 69 longitudinally extensive transverse myelitis lesions, while the remaining 11 (14.5%) had a total of 15 STM lesions. Of the 15 STM lesions, 5 spanned 2.5 vertebral segments, 6 were continuous over two segments, 3 showed a length of 1.5 segments and 1 was confined to a single segment. On axial imaging, all of the STM lesions involved the central grey matter.

Conclusion: These MRI findings suggested that STM does not preclude the possibility of an NMOSD diagnosis.

Keywords: Transverse myelitis; magnetic resonance imaging; neuromyelitis optica; neuromyelitis optica spectrum disorders; spinal cord.

MeSH terms

  • Adolescent
  • Adult
  • Aged
  • Aquaporin 4 / immunology
  • Autoantibodies / metabolism
  • Diagnosis, Differential
  • Early Diagnosis
  • Female
  • Humans
  • Magnetic Resonance Imaging / methods
  • Male
  • Middle Aged
  • Myelitis, Transverse / diagnosis
  • Myelitis, Transverse / pathology*
  • Neuromyelitis Optica / diagnosis*
  • Neuromyelitis Optica / pathology*
  • Spinal Cord / pathology
  • Spinal Cord Diseases / diagnosis
  • Spinal Cord Diseases / pathology
  • Young Adult

Substances

  • AQP4 protein, human
  • Aquaporin 4
  • Autoantibodies