Familial hemifacial spasm of young-onset: Report of two cases

J Neurol Sci. 2017 Feb 15:373:83-85. doi: 10.1016/j.jns.2016.12.034. Epub 2016 Dec 21.

Abstract

Hemifacial spasm (HFS) is defined as an involuntary twitching of the hemifacial muscles supplied by the facial nerve. It is mostly attributed to a vascular compression with the facial nerve. Familial HFS has been described in less than 10% of cases of sporadic HFS and usually develops after the age of 40. Young-onset HFS is a rare condition, generally presenting prior to the age of 30 with an estimated prevalence of 6.5% of sporadic HFS. No familial component has been described in small series of young-onset HFS. Here we report the cases of a patient and his mother who both developed right HFS in their early twenties. Both patients had a neurovascular contact between their right facial nerve and a branch of their right posterior inferior cerebellar artery. Our report explores how young-onset familial HFS may be the consequence of hereditary vascular variations.

Keywords: Botulinum toxin; Familial; Hemifacial spasm; Posterior inferior cerebellar artery; Young onset.

Publication types

  • Case Reports
  • Letter

MeSH terms

  • Age of Onset
  • Arteries / diagnostic imaging*
  • Cerebellum / blood supply*
  • Cerebellum / diagnostic imaging
  • Facial Nerve / diagnostic imaging*
  • Facial Nerve / surgery
  • Female
  • Hemifacial Spasm / diagnostic imaging*
  • Hemifacial Spasm / drug therapy
  • Hemifacial Spasm / etiology*
  • Hemifacial Spasm / surgery
  • Humans
  • Male
  • Nerve Compression Syndromes / complications
  • Nerve Compression Syndromes / diagnostic imaging
  • Nerve Compression Syndromes / drug therapy
  • Nerve Compression Syndromes / surgery
  • Young Adult

Supplementary concepts

  • Hemifacial Spasm, Familial