Metastatic Neuroendocrine Carcinoma of Unknown Origin Arising in the Femoral Nerve Sheath

World Neurosurg. 2017 Aug:104:1047.e1-1047.e6. doi: 10.1016/j.wneu.2017.05.013. Epub 2017 May 11.

Abstract

Background: Metastatic neuroendocrine carcinoma of unknown origin is a rare condition, usually presenting with lesions in the liver and/or lung. We present the first reported case of a metastatic neuroendocrine carcinoma of unknown origin arising in the femoral nerve sheath.

Case description: Magnetic resonance imaging demonstrated what was thought to be a schwannoma in the left femoral nerve sheath in the proximal femoral triangle, immediately inferior to the anterior inferior iliac spine. At the time of operation, the tumor capsule was invading surrounding tissue, as well as three trunks of the femoral nerve. The patient underwent a subtotal resection, preserving the integrity of the residual functioning femoral nerve trunks. Histologic evaluation determined that the tumor had features consistent with a metastatic neuroendocrine carcinoma of unknown primary origin. The patient recovered well postoperatively, and subsequent radiologic evaluation failed to demonstrate a potential primary site. Unfortunately, the patient re-presented with disease progression and was subsequently referred to palliative care.

Conclusions: We recommend that there is a definite role for surgery in the management of solitary neuroendocrine carcinoma of unknown origin.

Keywords: Carcinoma of unknown origin; Neuroendocrine carcinoma; Peripheral nerve sheath tumor.

Publication types

  • Case Reports

MeSH terms

  • Antineoplastic Combined Chemotherapy Protocols / therapeutic use
  • Bone Neoplasms / secondary
  • Carboplatin / administration & dosage
  • Carcinoma, Neuroendocrine / diagnostic imaging
  • Carcinoma, Neuroendocrine / secondary*
  • Carcinoma, Neuroendocrine / surgery
  • Chemotherapy, Adjuvant
  • Etoposide / administration & dosage
  • Female
  • Femoral Nerve*
  • Fluorodeoxyglucose F18
  • Humans
  • Lung Neoplasms / secondary
  • Magnetic Resonance Imaging
  • Middle Aged
  • Neoplasm Recurrence, Local / radiotherapy
  • Neoplasms, Unknown Primary / diagnostic imaging*
  • Nerve Sheath Neoplasms / diagnostic imaging
  • Nerve Sheath Neoplasms / secondary*
  • Nerve Sheath Neoplasms / surgery
  • Palliative Care
  • Positron Emission Tomography Computed Tomography
  • Radiopharmaceuticals

Substances

  • Radiopharmaceuticals
  • Fluorodeoxyglucose F18
  • Etoposide
  • Carboplatin