B Cell Anomalies in Autoimmune Retinopathy (AIR)

Invest Ophthalmol Vis Sci. 2017 Jul 1;58(9):3600-3607. doi: 10.1167/iovs.17-21704.

Abstract

Purpose: Autoimmune retinopathy (AIR) is a retinopathy associated with unexplained vision loss presumably linked to circulating antiretinal antibodies; currently, however, there are no standardized criteria regarding the diagnosis, treatment strategy, or pathogenesis of this disease. The importance of B-lymphocyte immunophenotyping in the classification of AIR is unknown.

Methods: We utilized 15-color multiparametric flow cytometry to identify aberrations in B cell subsets that may contribute to the pathophysiology of AIR. Luminex cytokine analysis was also performed on plasma samples from AIR patients.

Results: Significant differences in AIR patients compared to individuals with other inflammatory conditions or healthy donors were found in the B cell memory compartment, including an increase in naïve B cells and a decrease in switched and unswitched memory B cells, which correlated with alterations in immunoglobulin secretion.

Conclusions: These findings suggest that the maturation process of B cells may be impaired and that B cell immunophenotyping may help in understanding disease process in AIR.

Publication types

  • Research Support, N.I.H., Intramural

MeSH terms

  • Adult
  • Aged
  • Aged, 80 and over
  • Autoantibodies / blood
  • Autoantigens / immunology
  • Autoimmune Diseases / immunology*
  • Autoimmune Diseases / pathology
  • B-Lymphocyte Subsets / immunology*
  • B-Lymphocyte Subsets / pathology
  • Cytokines / blood
  • Electroretinography
  • Female
  • Flow Cytometry
  • Healthy Volunteers
  • Humans
  • Immunophenotyping
  • Male
  • Middle Aged
  • Panuveitis / blood
  • Retina / immunology
  • Retinal Diseases / immunology*
  • Retinal Diseases / pathology
  • Uveitis, Posterior / blood
  • Vision Disorders / diagnosis
  • Visual Fields

Substances

  • Autoantibodies
  • Autoantigens
  • Cytokines