Metastatic Solitary Fibrous Tumor With Doege-Potter Syndrome: Hypoglycemia Treated by 90Y Radioembolization

Clin Nucl Med. 2018 Mar;43(3):e93-e95. doi: 10.1097/RLU.0000000000001944.

Abstract

Solitary fibrous tumor is a rare type of mesenchymal neoplasm that can be associated to a paraneoplastic severe hypoglycemia due to the overproduction of insulinlike growth factor type 2: Doege-Potter syndrome. When surgical resection is impossible or unsuccessful, alternative therapies were described with heterogeneous efficiency. We report the use of radioembolization with Y-labeled glass microspheres in this application. Regarding the excellent results obtained and the potential interest of peptide receptor radionuclide therapy suggested by overexpression of somatostatin receptors in our patient, the place of targeted radionuclide therapies deserves to be explored in this group of tumors.

Publication types

  • Case Reports

MeSH terms

  • Humans
  • Hypoglycemia / complications*
  • Hypoglycemia / radiotherapy*
  • Male
  • Middle Aged
  • Neoplasm Metastasis
  • Solitary Fibrous Tumors / complications*
  • Solitary Fibrous Tumors / pathology*
  • Yttrium Radioisotopes / therapeutic use*

Substances

  • Yttrium Radioisotopes
  • Yttrium-90