Complement factor H protects mice from ischemic acute kidney injury but is not critical for controlling complement activation by glomerular IgM

Eur J Immunol. 2018 May;48(5):791-802. doi: 10.1002/eji.201747240. Epub 2018 Feb 22.

Abstract

Natural IgM binds to glomerular epitopes in several progressive kidney diseases. Previous work has shown that IgM also binds within the glomerulus after ischemia/reperfusion (I/R) but does not fully activate the complement system. Factor H is a circulating complement regulatory protein, and congenital or acquired deficiency of factor H is a strong risk factor for several types of kidney disease. We hypothesized that factor H controls complement activation by IgM in the kidney after I/R, and that heterozygous factor H deficiency would permit IgM-mediated complement activation and injury at this location. We found that mice with targeted heterozygous deletion of the gene for factor H developed more severe kidney injury after I/R than wild-type controls, as expected, but that complement activation within the glomeruli remained well controlled. Furthermore, mice that are unable to generate soluble IgM were not protected from renal I/R, even in the setting of heterozygous factor H deficiency. These results demonstrate that factor H is important for limiting injury in the kidney after I/R, but it is not critical for controlling complement activation by immunoglobulin within the glomerulus in this setting. IgM binds to glomerular epitopes after I/R, but it is not a significant source of injury.

Keywords: Complement; Factor H; IgM; Ischemia; Kidney.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Acute Kidney Injury / genetics
  • Acute Kidney Injury / pathology*
  • Animals
  • Complement Activation / immunology*
  • Complement Factor H / deficiency*
  • Complement Factor H / genetics
  • Complement Factor H / immunology*
  • Complement Pathway, Alternative / immunology
  • Epitopes / immunology
  • Hereditary Complement Deficiency Diseases
  • Immunoglobulin M / deficiency
  • Immunoglobulin M / immunology*
  • Kidney Diseases / genetics
  • Kidney Diseases / immunology*
  • Kidney Glomerulus / immunology*
  • Kidney Glomerulus / pathology
  • Mice
  • Mice, Inbred C57BL
  • Mice, Knockout
  • Reperfusion Injury / immunology*
  • Reperfusion Injury / pathology

Substances

  • Epitopes
  • Immunoglobulin M
  • Complement Factor H

Supplementary concepts

  • Complement Factor H Deficiency