The protein histidine phosphatase LHPP is a tumour suppressor

Nature. 2018 Mar 29;555(7698):678-682. doi: 10.1038/nature26140. Epub 2018 Mar 21.

Abstract

Histidine phosphorylation, the so-called hidden phosphoproteome, is a poorly characterized post-translational modification of proteins. Here we describe a role of histidine phosphorylation in tumorigenesis. Proteomic analysis of 12 tumours from an mTOR-driven hepatocellular carcinoma mouse model revealed that NME1 and NME2, the only known mammalian histidine kinases, were upregulated. Conversely, expression of the putative histidine phosphatase LHPP was downregulated specifically in the tumours. We demonstrate that LHPP is indeed a protein histidine phosphatase. Consistent with these observations, global histidine phosphorylation was significantly upregulated in the liver tumours. Sustained, hepatic expression of LHPP in the hepatocellular carcinoma mouse model reduced tumour burden and prevented the loss of liver function. Finally, in patients with hepatocellular carcinoma, low expression of LHPP correlated with increased tumour severity and reduced overall survival. Thus, LHPP is a protein histidine phosphatase and tumour suppressor, suggesting that deregulated histidine phosphorylation is oncogenic.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Carcinoma, Hepatocellular / enzymology
  • Carcinoma, Hepatocellular / pathology
  • Disease Models, Animal
  • Histidine / metabolism*
  • Humans
  • Inorganic Pyrophosphatase / deficiency
  • Inorganic Pyrophosphatase / genetics
  • Inorganic Pyrophosphatase / metabolism*
  • Liver Neoplasms / enzymology*
  • Liver Neoplasms / pathology*
  • Male
  • Mice
  • Phosphorylation
  • Proteomics
  • Survival Analysis
  • TOR Serine-Threonine Kinases / metabolism
  • Tumor Burden
  • Tumor Suppressor Proteins / deficiency
  • Tumor Suppressor Proteins / genetics
  • Tumor Suppressor Proteins / metabolism*

Substances

  • Tumor Suppressor Proteins
  • Histidine
  • MTOR protein, human
  • TOR Serine-Threonine Kinases
  • Inorganic Pyrophosphatase
  • phospholysine phosphohistidine inorganic pyrophosphate phosphatase, human