Papular epidermal nevus with "skyline" basal cell layer is a variant of keratinocytic nevus that usually occurs sporadically but may affect different family members. We report on the fourth family with papular epidermal nevus with "skyline" basal cell layer affecting a 3-month-old girl and her father.
Keywords: epidermal nevus; papular epidermal nevus with “skyline” basal cell layer; papular epidermal nevus with “skyline” basal cell layer syndrome; paradominant inheritance.
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