Role of β2/3-specific GABA-A receptor isoforms in the development of hippocampus kindling epileptogenesis

Epilepsy Behav. 2018 May:82:57-63. doi: 10.1016/j.yebeh.2018.02.020. Epub 2018 Mar 26.

Abstract

Objective: Subunit-specific positive allosteric modulators (PAMs) of gamma-aminobutyric acid-A (GABA-A) receptors are commonly used to uncover the role of GABA-A receptor isoforms in brain function. Recently, we have designed novel PAMs selective for β2/3-subunit containing GABA-A receptors (β2/3-selective PAMs) that are nonbenzodiazepine site-mediated and do not show an α-subunit isoform selectivity, yet exhibit anxiolytic efficacy with reduced potential for sedation, cognitive impairment, and tolerance. In this study, we used three novel β2/3-selective PAMs (2-261, 2-262, and 10029) with differential β2/3-subunit potency to identify the role of β2/3-selective receptor isoforms in limbic epileptogenesis.

Methods: Experimental epileptogenesis was induced in mice by daily hippocampus stimulations until each mouse showed generalized (stage 5) seizures. Patch-clamp electrophysiology was used to record GABA-gated currents. Brain levels of β2/3-selective PAMs were determined for mechanistic correlations.

Results: Treatment with the β2/3-selective PAMs 2-261 (30mg/kg), 2-262 (10mg/kg), and 10029 (30mg/kg), 30min prior to stimulations, significantly suppressed the rate of development of kindled seizure activity without affecting the afterdischarge (AD) signal, indicating their disease-modifying activity. The β2/3-selective agents suppressed chemical epileptogenesis in the pentylenetetrazol model. Test doses of these agents were devoid of acute antiseizure activity in the kindling model.

Conclusion: These findings demonstrate that β2/3-selective PAMs can moderately retard experimental epileptogenesis, indicating the protective role of β2/3-subunit GABA-A receptor isoforms in the development of epilepsy.

Keywords: Allosteric modulator; Epileptogenesis; GABA; Ganaxolone; Kindling; Subunit-specific.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Allosteric Regulation / drug effects
  • Allosteric Regulation / physiology
  • Animals
  • Epilepsy / drug therapy*
  • Epilepsy / physiopathology*
  • GABA Modulators / pharmacology
  • GABA Modulators / therapeutic use*
  • Hippocampus / drug effects
  • Hippocampus / physiopathology*
  • Kindling, Neurologic / drug effects
  • Kindling, Neurologic / physiology*
  • Male
  • Mice
  • Mice, 129 Strain
  • Mice, Inbred C57BL
  • Protein Isoforms
  • Receptors, GABA-A / physiology*
  • Seizures / physiopathology
  • Temporal Lobe / drug effects
  • Temporal Lobe / physiopathology

Substances

  • GABA Modulators
  • Protein Isoforms
  • Receptors, GABA-A